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ARVC Task Force Criteria (2010 Revised) Calculator

  • Global or Regional Dysfunction and Structural Alterations (RV imaging)
  • Repolarization Abnormalities (ECG)
  • Depolarization/Conduction Abnormalities (ECG)
  • Arrhythmias
  • Family History
  • Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) Task Force Criteria (2010 Revised): Explanation and Clinical Context
    The ARVC Task Force Criteria (2010 revised) is a structured diagnostic tool used to improve diagnostic accuracy for ARVC, a genetic cardiomyopathy characterized by fibro-fatty replacement of the right ventricular myocardium, leading to arrhythmias and sudden cardiac death.
    The criteria are divided into six categories: global or regional dysfunction and structural alterations (assessed by imaging), repolarization abnormalities, depolarization/conduction abnormalities (ECG), arrhythmias, histopathology (if available), and family history/genetics. Each category is scored as major or minor based on specific quantitative and qualitative thresholds.
    Diagnosis is determined by combining major and minor criteria: Definite ARVC (2 major, or 1 major + 2 minor, or 4 minor), Borderline ARVC (1 major + 1 minor), Possible ARVC (2 minor).
    These criteria are widely used in clinical practice for risk stratification, early diagnosis, and guiding family screening and management.

    Reference:
    Marcus FI, McKenna WJ, Sherrill D, et al. Diagnosis of Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia: Proposed Modification of the Task Force Criteria. Circulation. 2010;121:1533–1541. doi:10.1161/CIRCULATIONAHA.109.849029